ISSN: 1305-385X
Hakkında: Özel sayılar şeklinde yayınlanır.
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Restrictive Cardiomyopathy
Dr. Güllü ÖZALPa, Dr. H. Asuman KAFTANa
aKardiyoloji ABD, Pamukkale Üniversitesi Tıp Fakültesi Kalp Merkezi, DENİZLİ
World Health Organization and World Health Fund define cardiomyopathies as the heart muscle disease of unknown cause and classify them by the hemodynamic and pathophysiologic criteria. This classification separates primary myocardial diseases from the secondary processes such as ischemic, hypertensive, valvular or congenital causes, however, it is still debated despite the revisions.
The clinicopathologic classification which is offered br Goodwin is similar to the WHO classification and includes dilated, hypertrophic and restrictive forms. Restrictive cardiomyopathy is characterized by restrictive filling and reduced diastolic volume of either or both ventricles with normal or near-normal systolic function and wall thickness. This situation may be idiopathic or due to systemic myocardial disorder. So, the clinical and hemodynamic findings mimic the constrictive pericarditis and characterized by a increased jugular venous pressure with rapid X and Y descents, small or normal ventricular sizes and pulmonary congestion. Restrictive cardiomyopathy may be infiltrative or noninfiltrative, may be with or without obstruction. If it is due to infiltration it may be interstitial (amyloid, sarcoid) or cellular(hemochromatosis).Keywords: Restrictive cardiomyopathy,diastolic dysfunctionTurkiye Klinikleri J Int Med Sci 2007, 3(24):26-33
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